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川崎氏病 - Wikipedia

川崎氏病

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川崎氏病(Kawasaki disease),又稱為川崎病黏膜皮膚淋巴腺症候群(mucocutaneous lymphnode syndrome),是屬於幼兒期的一種急性疾病。此病是由日本小兒科醫師川崎富作於西元1967年首先提出報告,故名之為川崎氏病。

目录

[编辑] 流行病學

此病好發於五歲以下小孩。

[编辑] 臨床症狀

[编辑] 病因

川崎氏病的病因依舊未明,但許多科學家懷疑這可能是一種特殊的病毒感染導致。目前傾向於把他當成是一種與免疫系統有關的疾病。

[编辑] 治療

因為病因未明,所以此病沒有針對病原的特殊療法。急性期常合併使用靜脈注射高劑量免疫球蛋白與高劑量阿斯匹靈(Aspirin)(60 mg/kg/day),退燒後改使用低劑量的阿斯匹靈(10/mg/kg/day)。如已併發冠狀動脈瘤形成的病患,則需要繼續長期追蹤治療。

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